Popliteal pterygium syndrome is rare, with 60 cases described in the literature. The syndrome includes a popliteal who extending from the ischium to the heel and other abnormalities including toenail dysplasia, deformities of the foot and toes,
and
oral
cavity abnormalities. The main orthopedic problem is a flexion contracture of the knee and an equinus foot. We experienced a six-month-old girl with popliteal pterygium, in whom resection of abnormal fibrotic muscle belly, Achilles tendon
legnthening,
and Z-plastic lengthening of the skin resulted partial correction of flexion deformity of the knee and equinus contracture of the foot at one year follow-up.
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